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- Disease Information
- Disease Comparison
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Disease Processes ▼
- Auto Immune
- Vascular-Arteriosclerosis
- Biochemical
- Congenital-developmental
- Deficiency
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Major Organs-Systems ▼
- Systemic
- Pediatric
- Nervous & Sensory System (Neurology)
- Cardiovascular System
- Respiratory (Pulmonary) System
- Gastro-Intestinal (Digestive) System
- Urinary System
- Dermatologic System
- Endocrine System
- Immune System
- Musculoskeletal System
- Genital Reproductive System
- Hematopoietic System (Hematology)
- Lymphatic System
- Tissue/Cells/Organelles
Disease Information for Urticaria pigmentosa
- Clinical Manifestations
- Signs & Symptoms
- Brown skin discoloration
- Darier's sign/hive with scratch/papule
- Excoriations
- Flushing
- Hemorrhagic rash
- Hemorrhagic/Confluent ecchymotic rash
- Increased pigmentation/tanning/hyperpigmented
- Itching after hot bath
- Pruritic/itching rash
- Pruritis Itching
- Rash
- Rash/Characteristic pattern/distribution
- Subepidermal Blisters
- Urticaria, nonallergic/symptomatic
- Chronic Diarrhea in a Child
- Clinical Presentation & Variations
- Presentation/ Papular Rash Face Upper Arms
- Disease Progression
- Course/Chronic disorder
- Course/Chronic only
- Course/Self limited usually
- Course/Usually spontaneous remission/2-3 years
- Demographics & Risk Factors
- Population Group
- Child
- Infant
- Population/Pediatrics population
- Sex & Age Groups
- Population/Child
- Population/Children/all
- Population/Infant
- Laboratory Tests
- Abnormal Lab Findings - Decreased
- Complement (total CH50) level (Lab)
- Abnormal Lab Findings - Increased
- Beta Tryptase, Serum (Lab)
- CarboxyPeptidase A (CPA)
- Heparin serum level/intrinsic (Lab)
- Histamine (Lab)
- Tryptase, serum (Lab)
- URINE Histamine
- URINE Histamine metabolites
- Diagnostic Test Results
- Pathology
- BX/Skin biopsy/Abnormal
- BX/Skin Mast cells/clustered
- PATH/Mast cell tissue infiltrates
- Associated Diseases & Rule outs
- Rule Outs
- Anaphylaxis, generalized
- Angioedema/angioneurotic edema
- Carcinoid syndrome/metastatic carcinoid
- Smallpox
- Urticaria/hives
- Associated Disease & Complications
- Chronic hives/urticaria
- Dermatitis/Chronic rash
- Dermatographism (Darier's Sign)
- Hyperpigmentation
- Mastocytosis, systemic
- Telangiectasia
- Urticaria pigmentosa
- Urticaria/hives
- Disease Mechanism & Classification
- Class
- CLASS/Pediatric disorders (ex)
- CLASS/Mast cell involvement/disorder (ex)
- Pathophysiology
- Pathophysiology/Basophile degranulation process
- Pathophysiology/Histamine cellular release
- Pathophysiology/Mast cell degranulation/activation
- Process
- PROCESS/Benign condition (ex)
- PROCESS/Bimodal age distribution/incidence
- PROCESS/Hypertrophic/Hyperplastic disorder (ex)
- Synonyms
- Synonym
- Cutaneous Mastocytoses Maculopapular, Cutaneous Mastocytosis Maculopapular, Localised cutaneous mastocytosis, Localized cutaneous mastocytosis, Maculopapular Cutaneous Mastocytoses, Maculopapular Cutaneous Mastocytosis, pigmentation congenital urticaria pigmentosa, pigmentosa urticaria, UP MPCM, urticaria pigmentosa, Urticaria pigmentosa (disorder), Urticaria Pigmentosa Maculopapular Cutaneous Mastocytosis, Synonym/Localized infantile mastocytosis, Synonym/Mastocytosis, infantile, Synonym/Nettleships/E disease type 1, Synonym/Urticaria perstans hemorrhagica, Synonym/Xanthalasmoidea
- Treatment
- Drug Therapy - Indication
- RX/Diphenhydramine (Benadryl)
- RX/Oral Cromolyn (cromoglycate)
- Surgical Procedures or Treatments
- SX/Biopsy
- Definition
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The most common form of mastocytosis. It occurs primarily in children and is typically characterized by multiple persistent small, reddish-brown, hyperpigmented, pruritic macules and papules. They are located most commonly on the trunk, but seen also on the extremities, head, and neck. (Dorland, 27th ed)
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- External Links Related to Urticaria pigmentosa
- Wikipedia
- Merck
- Images
- PubMed (National Library of Medicine)
- NGC (National Guideline Clearinghouse)
- Medscape (eMedicine)
- Harrison's Online (accessmedicine)
- NEJM (The New England Journal of Medicine)