Disease Information for Splenomegaly, congestive, chronic

Banti"s Syndrome; Banti"s Disease; Hypersplenism;

Banti syndrome is a disorder of the spleen; In the case of Banti syndrome, the spleen rapidly but prematurely destroys blood cells; This syndrome is characterized by abnormal enlargement of the spleen (splenomegaly) due to obstruction of blood flow in some veins and abnormally increased blood pressure (hypertension) within the veins of the liver (eg, hepatic or portal veins) or the spleen (splenic veins); The disorder may be due to any number of different factors causing obstruction of portal, hepatic, or splenic veins including abnormalities present at birth (congenital) of such veins, blood clots, or various underlying disorders causing inflammation and obstruction of veins (vascular obstruction) of the liver----------[NORD 2005]------------

Banti"s disease Also known as: Banti"s syndrome; Banti-Senator disease; Senator syndrome; Chronic congestive splenomegaly, cirrhotic splenomegaly, congestive splenomegaly, fibrocongestive splenomegaly, hepatolienal fibrosis, nonfamilial splenic anaemia, spleen-liver syndrome, splenic anaemia; A syndrome of anemia, congestive splenic enlargement, thrombocytopenia, leukopenia, gasterointestinal hemorrhages, portal cirrhosis, obstruction of splenic, portal, or intrahepatic veins and ultimately cirrhosis of liver; Epitaxis in 30 % of cases; Considered secondary to portal hypertension; May occur in childhood, most frequently in females under 35 years of age, and affects either sex; Insidious or sudden onset; There is some disagreement among authors as to the terms Banti"s disease and Banti"s syndrome---------[whonamedit_com 2005]----------

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