Disease Information for Scimitar syndrome

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Clinical Manifestations
Signs & Symptoms
Cardiac Symptoms/Signs
Graham Steell murmur/diastol (functional pulm insuffic)
P2 sound accentuated
Right ventricular heave
Recurrent URI/Colds/LRI infections
Asymptomatic patient
Clinical Presentation & Variations
Presentation/Recurrent respiratory infections
Presentation/Congenital Heart Disease in Adults
Presentation/Pneumonia Chronic Persistent
Presentation/Recurrent pneumonia Child
Disease Progression
Course/Chronic disorder
Course/Chronic only
Demographics & Risk Factors
Population Group
Child
Population/Pediatrics population
Young Adult
Sex & Age Groups
Population/Adult/all
Population/Child
Population/Children/all
Population/Young adult
Diagnostic Test Results
Other Tests & Procedures
Heart Cath/Left to Right Shunt
Heart cath/Right ventricle end diastolic/high
Jugular venous tracing/a wave prominent
EKG (ECG)
EKG/Incomplete right bundle branch block (ECG)
EKG/Normal (ECG)
X-RAY
Fluoroscopy/Cardiac/Chest abnormal
Xray/Chest abnormal
Xray/Heart position/abnormal/Chest
Xray/Chest film/extrapulmonary abnormal
Xray/Chest/Lung fields/Abnormal
Xray/Hypoplastic right lung/hyperaerated left/Chest
Xray/Left pulmonary artery lrg/hypoplastic Rgt/Chest
Xray/Mediastinal shift/Chest
Xray/Pulm arteries dilated/distal narrow/Chest
Xray/Pulmonary arteries central dilation/Chest
Xray/Right lower lobe disorder/Chest
Xray/Scimitar pattern/right heart border/Chest
Xray/Segmental hyperlucency/Chest
Xray/Unilateral hyperlucent lung/Chest
Ultrasound
Echo/Pulmonary artery hypertension
Echo/Right Atrium Chamber Large
Echo/Right atrium increased volume/diameter
Angiography
Angios/Neck vessels/Arch study/abnormal
Angios/Right atrium enlarged/Heart
Heart cath/Abnormal
Heart cath/Left right shunt/O2 curve
Heart cath/Oxygen curve/stepup vena cava
Associated Diseases & Rule outs
Associated Disease & Complications
Atrial septal defect
Bacterial endocarditis/acute
Bronchiectasis
Bronchitis, chronic
Dextrocardia
Eisenmenger's syndrome/pulmonary hypertension
Pneumonia, recurrent
Pneumonia/Bronchopneumonia
Pulmonary hypertension, secondary
Right ventricular hypertrophy
Scimitar syndrome
Disease Mechanism & Classification
Class
CLASS/Cardiovascular (category)
CLASS/Great vessels disorder (ex)
CLASS/Heart disorder (ex)
Pathophysiology
Pathophysiology/Anomalous arterial communications/chest
Pathophysiology/Anomalous rt pulmonary vein/vena cava
Pathophysiology/Left to right cardiac shunt
Pathophysiology/Defective development right lung
Process
PROCESS/Congenital/developmental (category)
PROCESS/Congenital heart disease (ex)
PROCESS/Shunt/left to right/congenital
PROCESS/Anomalies/Deformities/Malformations (EX)
PROCESS/Acyanotic congenital heart disease (ex).
Synonyms
Synonym
ANOMALOUS PULMONARY VENOUS RETURN, APVR, SCIMITAR ANOMALY, Scimitar syndrome, Scimitar syndrome (disorder), Syndrome Scimitar, TAPVR1, TOTAL ANOMALOUS PULMONARY VENOUS RETURN 1, Synonym/Anomalous drainage/pulmonary veins/IVC, Synonym/Hypogenic lung syndrome, Synonym/Turkish sabre syndrome, Synonym/Venolobar/scimitar syndrome
Definition

Anomalous venous drainage of the right lung into the inferior vena cava, with hypoplasia of the right lung. The scimitar-shaped radiographic shadow of the anomalous vein gives the syndrome its name.

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External Links Related to Scimitar syndrome
Google
Wikipedia
Merck
Images
PubMed (National Library of Medicine)
NGC (National Guideline Clearinghouse)
Medscape (eMedicine)
Harrison's Online (accessmedicine)
NEJM (The New England Journal of Medicine)
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