Disease Information for Pemphigoid, bullous

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Clinical Manifestations
Signs & Symptoms
Red/erythema skin discoloration
Blisters
Bulla/bullous rash
Bullous rash/spares mucosa
Erosions
Erythroderma
Genital rash/lesion
Grouped Lesions Rash
Lesions/rash extremities distribution
Nikolskys sign
Pruritic/itching rash
Rash
Rash/Lesions occur on pressure points/Acral lesions
Skin sloughing/denuded/raw/oozing areas
Subepidermal Blisters
Vesicobullous rash in Elderly
Vesicobullous rash/lesions in Children
Vesicobullous rashes
Vesicular rash
Genital Erosions
Oral erythematous lesion
Oral lesion/ulcer
Oral Mucosal Erosive Lesions
Oral Mucosal Punctate Lesions
Oral Ulcers in Elderly
Oral Vesicles
Oral/pharyngeal slough/blisters/mucositis
Stomatitis Blisters/blebs
Vulva Erosions
Laboratory Tests
Abnormal Lab Findings (Non Measured)
Anti-BP 180 test/Blood (labs)
Anti-BP 230 test/blood (labs)
Abnormal Lab Findings - Increased
Anti-basement membrane (BMZ/EBA/Collagen iv) skin
IGE/Immunoglobulin E (Lab)
Diagnostic Test Results
Pathology
BX/Skin biopsy/Abnormal
BX/Skin biopsy/Epidermal fluorescent antibody
BX/Skin biopsy/fluorescent antibody abnormal
Associated Diseases & Rule outs
Rule Outs
Angioedema/angioneurotic edema
Behcet's syndrome
Chronic hives/urticaria
Dermatitis herpetiformis
Impetigo/Pyoderm
Pemphigus
Stevens-Johnson syndrome
Urticaria/hives
Associated Disease & Complications
Bullous Stomatitis
Pemphigoid, bullous
Staphylococcus aureus infection
Disease Mechanism & Classification
Class
CLASS/Dermatologic/Subcutaneous (category)
Pathophysiology
Pathophysiology/Antigen skin basement membrane
Pathophysiology/Burn/extensive
Pathophysiology/Skin surface/denuded areas
Process
PROCESS/Allergy/collagen/autoimmune (category)
PROCESS/Autoimmune disorder (ex)
PROCESS/Reference organ/system (category)
Synonyms
Synonym
BP Bullous pemphigoid, bullous pemphigoid, Bullous pemphigoid (disorder), PEMPHIGOID, Pemphigoid (disorder), Pemphigoid Bullous, Pemphigoid unspecified, Pemphigoids, Synonym/BP (Bullous Pemphigoid)
Definition

A chronic and relatively benign subepidermal blistering disease usually of the elderly and without histopathologic acantholysis;-----------------------------------------.

Mucous Membrane Pemphigoid; CP; Cicatricial Pemphigoid; MMP; Mucous Membrane Pemphigoid ; Subdivisions: Brunsting-Perry Syndrome; Localized Cicatricial Pemphigoid; Vegetating Cicatricial Pemphigoid; Mucous membrane pemphigoid (MMP) is a rare group of chronic autoimmune disorders characterized by blistering lesions that primarily affect the various mucous membranes of the body; The mucous membranes of the mouth and eyes are most often affected; The mucous membranes of the nose, throat, genitalia, and anus may also be affected; The symptoms of MMP vary among affected individuals depending upon the specific site(s) involved and the progression of the disease; Blistering lesions eventually heal, sometimes with scarring; Progressive scarring may potentially lead to serious complications affecting the eyes and throat; In some cases, blistering lesions also form on the skin, especially in the head and neck area; The exact cause of MMP is unknown; Mucous membrane pemphigoid has been known by many different names within the medical literature including benign mucous membrane pemphigoid, cicatricial (scarring) pemphigoid, and ocular cicatricial pemphigoid; In March of 2002, a consensus group of researchers determined that mucous membrane pemphigoid was the best designation for this group of disorders; The term "benign" mucous membrane pemphigoid was deemed inappropriate because of the potential for serious complications in some cases; The term "cicatricial" pemphigoid excluded affected individuals who do not develop scarring; Site-specific terms such as "ocular" cicatricial pemphigoid excluded individuals with multiple site involvement;[NORD]

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External Links Related to Pemphigoid, bullous
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Harrison's Online (accessmedicine)
NEJM (The New England Journal of Medicine)
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