- Differential Diagnosis
- Diseases
- Drugs
- More
-
- Try building your search one term at a time, and be as specific as you can! Search term example: "chronic cough".
- Do not enter multiple findings such as "anemia, chronic cough, weight loss, vomiting" all at the same time.
- After selecting your term from the search results a list of possible diagnoses will be generated. If the list is too long, you will be able to narrow it down by entering additional terms.
- Do not enter values such as "heart rhythm 110" or "sodium 125", instead use "tachycardia" or "hyponatremia".
- Disease Information
- Disease Comparison
-
Disease Processes ▼
- Auto Immune
- Vascular-Arteriosclerosis
- Biochemical
- Congenital-developmental
- Deficiency
- Degenrative-Necrosis
- Electromagnetic-Physics
- Eponymic
- Functional-Physiologic
- Hereditofamilial
- Iatrogenic
- Idiopathic
- Infected Organ-Abcess
- Infectious agent
- Inflammatory-Granulomatous
- Metabolic-Storage
- Neoplastic
- Poison Agent
- Poisoned Organ
- Radiation-Xray-trauma
- Mental
- Structural-Anatomic-Foreign body
- Surgical Procedure-Complication
- Trauma
- Use-age-Atrophic
- Endocrine-Vegetative
-
Major Organs-Systems ▼
- Systemic
- Pediatric
- Nervous & Sensory System (Neurology)
- Cardiovascular System
- Respiratory (Pulmonary) System
- Gastro-Intestinal (Digestive) System
- Urinary System
- Dermatologic System
- Endocrine System
- Immune System
- Musculoskeletal System
- Genital Reproductive System
- Hematopoietic System (Hematology)
- Lymphatic System
- Tissue/Cells/Organelles
Disease Information for Malignant histiocytosis
- Clinical Manifestations
- Signs & Symptoms
- Chest Pain
- Excess Sweating Children
- Fever and Rash
- Hyperhidrosis/Chronic sweating excess
- Purpura
- Rash
- Sweating Excess Perspiration
- Lymphadenopathy
- Lymphadenopathy Systemic
- Hepatosplenomegaly
- Palpable Liver/Hepatomegaly
- Weak/Weak as a kitten (symptom)
- Chest pain/non-cardiac
- Chest Wall Pain
- Acute Back Pain
- Back Pain
- Backache
- Splenomegaly
- Chronically ill patient/signs
- Enervated/extreme acute fatigue
- Fever
- Fever Febrile Possible
- Flu-Like Syndrome
- High body temperature
- Weakness
- Weakness non-neuromuscular/systemic
- Weight Loss
- Clinical Presentation & Variations
- Presentation/Lymphopenia Candidal diarrhea
- Disease Progression
- Course/Chronic only
- Course/Lethal
- Course/Prognosis bad/usually
- Course/Relentless
- Pancytopenia with Infiltrated Marrow
- Demographics & Risk Factors
- Family History
- Family history/Blood disease
- Sex & Age Groups
- Population/Adult/all
- Laboratory Tests
- Abnormal Lab Findings (Non Measured)
- Acute inflammatory markers elevated (Lab)
- Chronic lymphopenia
- Leukopenia
- Right Shift (Viral) Differential Smear (Lab)
- Abnormal Lab Findings - Decreased
- WBC
- Hematocrit (Lab)
- Hemoglobin (Lab)
- Lymphocytes (Lab)
- Platelet count (Lab)
- RBC/Red Blood Count (Lab)
- WBC/White Blood Cell Count/Leukocytes (Lab)
- Abnormal Lab Findings - Increased
- ACE/Angiotensin converting enzyme level (Lab)
- Lymphocytes (Lab)
- Diagnostic Test Results
- Pathology
- Bone marrow/Erythrophagocytosis
- Bone marrow/Histiocyte hypertrophy/infiltrate
- BX/Bone Marrow Biopsy/Abnormal
- BX/Lymph node biopsy/abnormal
- PATH/Histiocyte hypertrophy/infiltration tissue
- PATH/Erythrophagocytosis/Spleen
- PATH/Histiocyte hypertrophy/infiltrate spleen/nodes/RES
- Associated Diseases & Rule outs
- Rule Outs
- Mastoiditis
- Pancytopenia
- Associated Disease & Complications
- Anemia
- Candida albicans infection
- Lymphocytopenia
- Lymphocytosis
- Malignant histiocytosis
- Metastatic liver disease
- Thrombocytopenia
- Disease Mechanism & Classification
- Class
- CLASS/Langerhan Cell/Tissue Macrophages involvement/disorder (ex)
- CLASS/Hematologic (category)
- CLASS/Leukocyte involvement/disorder (ex)
- CLASS/Marrow involvement/disorder (ex)
- CLASS/Epiphyses Lesion/Involvement
- CLASS/Reticuloendothelial system (RES) disorder (ex)
- CLASS/Spleen/thymus/RES/immune system (category)
- Pathophysiology
- Pathophysiology/Histiocyte/macrophage disorder (ex)
- Pathophysiology/Bone marrow infiltration
- Pathophysiology/Decreased T Cells
- Pathophysiology/Immune/cellular system disorder (ex)
- Process
- PROCESS/Autosomal recessive disorder (ex)
- PROCESS/Hereditary/Genetic predisposition (ex)
- PROCESS/Hereditofamilial variant/pedigrees reported (ex)
- PROCESS/INCIDENCE/Rare disease (ex)
- PROCESS/Lymphomas (ex)
- PROCESS/Malignancy/cancer (ex)
- PROCESS/Neoplastic (category)
- PROCESS/Blood dyscrasia/leukemic process (ex)
- PROCESS/Leukemia process (ex).
- Synonyms
- Synonym
- Histiocyt medull reticulos, Histiocytic medullary reticul, Histiocytic Medullary Reticuloses, Histiocytic medullary reticulosis, Histiocytic medullary reticulosis (disorder), Histiocytic medullary reticulosis (morphologic abnormality), Histiocytic medullary reticulosis (obs), Histiocytoses Malignant, HISTIOCYTOSIS MALIGNANT, HMR, Malignant Histiocytoses, Malignant histiocytosis, Malignant histiocytosis (clinical), Malignant histiocytosis (disorder), Malignant histiocytosis (morphologic abnormality), Malignant histiocytosis RETIRED, Malignant midline reticulosis, Malignant reticuloendothelios, Malignant reticuloendotheliosis, Malignant reticulosis, Medullary Reticuloses Histiocytic, Medullary Reticulosis Histiocytic, Midline malignant reticulosis, Nasal T cell lymphoma, Polymorphic reticulosis, reticuloendotheliosis malignant, Reticuloses Histiocytic Medullary, RETICULOSIS ALEUKEMIC, RETICULOSIS HISTIOCYTIC MEDULLARY, RETICULOSIS MALIGNANT, RETICULOSIS MALIGNANT MIDLINE, reticulosis polymorphic, RETICULOSIS POLYMORPHORIC, Stewart's granuloma, Synonym/Familial hemophagic reticulosis, Synonym/Histiocytic leukemia, Synonym/Histiocytic medullary reticulosis, Synonym/Reticulosis, aleukemic, Synonym/Reticulosis, malignant
- Treatment
- Drug Therapy - Indication
- RX/Chemotherapy(cancer)
- Definition
-
A rare, usually rapidly progressive disorder, characterized by abrupt onset, fever, weight loss, hepato-splenomegaly, pancytopenia, and lymphadenopathy.
(Edit)
- External Links Related to Malignant histiocytosis
- Wikipedia
- Merck
- Images
- PubMed (National Library of Medicine)
- NGC (National Guideline Clearinghouse)
- Medscape (eMedicine)
- Harrison's Online (accessmedicine)
- NEJM (The New England Journal of Medicine)