Disease Information for Hip osteochondrosis/capital epiphysitis/LCP Dis

Legg Perthes disease;osteochondritis of femur head/hip pain; developmental------------------------------

Legg Calve Perthes Disease; LCPD; Perthes Disease; Legg-Calve-Perthes Disease (LCPD) is one of a group of disorders known as the Osteochondroses; The Osteochondroses typically are characterized by degeneration (avascular necrosis) and subsequent regeneration of the growing end of a bone (epiphyses); In Legg-Calve-Perthes Disease, the growing end (epiphysis) of the upper portion (capital) of the thigh bone (femur) is affected; Researchers believe that an unexplained interruption of the blood supply (ischemia) to the capital femoral epiphysis results in degeneration (avascular necrosis) and deformity of the thigh bone in this area; Symptoms may include a limp with or without pain in the hip, knee, thigh, and/or groin; muscle spasms; delayed maturation of the femur (delayed bone age); mild short stature; and/or limited movements of the affected hip; The disease process can be self-limiting as new blood supplies are established (revascularization) and new healthy bone forms (reossifies) in the affected area; Most cases of Legg-Calve-Perthes Disease occur randomly for no apparent reason (sporadically) [nord 2005]--------------------------------Also: Maydl’s disease; Perthes-Calvé-Legg-Waldenström syndrome; Waldenström"s syndrome; capital femoral epiphysis coxa plana, femoral osteochondrosis syndrome, osteoarthritis coxae, osteochondropathia deformans coxae juvenilis, osteochondritis deformans juvenilis, osteochondrosis of capitular epiphysis of femur;

Disorder characterized by unilateral or bilateral aseptic necrosis of the emphysis of the head of the femur (caput femoris); This is s a consquence of insufficient blood supply to the femur, and the tip of the bone dies over a period of 1 to 3 weeks; New blood supply causes new bone cells to appear in the region over the next 6 to 12 months; New bone then replaces the old bone within 2 to 3 years; The disease thus progresses from necrosis through revascularization, mottling, and fragmentation of the epiphysis to reossification and flattening of the head of the femur; There is moderate pain in the hip, with stiffness and restricted movement of the hip and a slight limp of involved leg;. The limp becomes worse as result of the atrophy and shortening of the femur; The sporadic type is unilateral in most instances and prevalent in in boys; sudden or gradual onset between 3 and 12 years (most commonly 5-10) of age; The hereditary type is transmitted as an autosomal dominant trait, and there is equal susceptibility of the sexes and a greater proportion of bilateral involvement; The condition was first described by Karel Maydl (1853-1903) in 1897; [whonamedit_com 2005]--------------

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