Disease Information for Hemangioblastoma

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Clinical Manifestations
Signs & Symptoms
Proptosis,unilateral
Disease Progression
Course/Chronic disorder
Course/Chronic only
Laboratory Tests
Abnormal Lab Findings (Non Measured)
Chromosomal abnormality (Lab)
Diagnostic Test Results
Ultrasound
Ultrasound/Liver/Vascular tumor mass
Disease Mechanism & Classification
Class
CLASS/Vascular disorder (ex).
Pathophysiology
Pathophysiology/Gene locus 3p25
Pathophysiology/Gene locus chromosome 3
Pathophysiology/Gene locus Chromosome 3p
Pathophysiology/Highly vascular tumor/cancer
Pathophysiology/Oncogene VHL/Locus 3p
Pathophysiology/Intramedullary Spinal Tumor
Process
PROCESS/Angioma (example)
PROCESS/Primary soft tissue tumor (ex)
PROCESS/Congenital neoplasm (ex)
Definition

A benign tumor of the nervous system that may occur sporadically or in association with HIPPEL-LINDAU DISEASE; It accounts for approximately 2% of intracranial tumors, arising most frequently in the cerebellar hemispheres and vermis; Histologically, the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial cells and clusters of lipid-laden pseudoxanthoma cells; Usually solitary, these tumors can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial compartment; Cerebellar hemangioblastomas usually present in the third decade with INTRACRANIAL HYPERTENSION, and ataxia----- (From DeVita et al, Cancer: Principles and Practice of Oncology, 5th ed, pp2071-2)-------

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External Links Related to Hemangioblastoma
Google
Wikipedia
Merck
Images
PubMed (National Library of Medicine)
NGC (National Guideline Clearinghouse)
Medscape (eMedicine)
Harrison's Online (accessmedicine)
NEJM (The New England Journal of Medicine)
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