Disease Information for Facial hemiatrophy, progressive (Parry-Romberg)

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Clinical Manifestations
Signs & Symptoms
Adolescent
Particular physiognomy/Odd looking kids
Cheeks Sunken/Wasting
Craniofacial Abnormalities/Congenital
Face atrophic/unilateral
Facial hemihypertrophy
Unilateral facial pain
Unilateral baldness/patchy
Unilateral carious/teeth
Unilateral facial hyperpigmentation
Unilateral facial vitiligo
Unilateral white hair/streak
White hair patches
Carious teeth/child
Carious teeth/sign
Delayed dentition/teething
Eroded teeth
Teeth malformed/dysplastic
Facial muscle wasting/sign
Jacksonian seizure
Seizures
Unilateral facial dysesthesias
Asymmetric body/build
Lateral Asymmetry
Unilateral eyelashes/eyebrow loss
Typical Clinical Presentation
Course/Onset early teens/progresses 5 years then stable
Clinical Presentation & Variations
Presentation/Multiple deformities newborn (odd look)
Disease Progression
Course/Chronic disorder
Course/Chronic only
Demographics & Risk Factors
Population Group
Child
Population/Pediatrics population
Sex & Age Groups
Population/Adolescent
Population/Adult ('twenties')
Population/Child
Population/Children/all
Population/Old child
Associated Diseases & Rule outs
Associated Disease & Complications
Atrophic glossitis/Glossitis
Convulsions (grand mal)
Dental caries
Dental deformities/anomalies
Epilepsy
Facial hemiatrophy, progressive
Hemihypertrophy
Migraine headache syndrome
Teeth enamel hypoplastic
Trigeminal neuralgia
Disease Mechanism & Classification
Class
CLASS/Pediatric disorders (ex)
CLASS/Primary organ/system disorder (ex)
CLASS/Area specific/facial/head/neck (category)
CLASS/Faces-cranio online database (ex)
CLASS/Facial area manifestation/disorder (ex)
CLASS/Neurologic (category)
Pathophysiology
Pathophysiology/Variable course subsets/severe/mild
Pathophysiology/Unilateral effects
Process
PROCESS/Atrophic disorders (ex)
PROCESS/Congenital/developmental (category)
PROCESS/Degenerative/necrosis disorder (category)
PROCESS/Idiopathic/unclassified/unknown (category)
PROCESS/Use/Age/atrophic disorder (category)
PROCESS/Dystostosis/craniofacial (ex)
Synonyms
Synonym
Atrophies Hemifacial, Atrophies Progressive Hemifacial, Atrophy Hemifacial, ATROPHY HEMIFACIAL ROMBERG, Atrophy Progressive Hemifacial, Disease Parry Romberg, Disease Romberg, Disease Romberg's, face hemiatrophy, FACE HEMIATROPHY PROGRESSIVE, Facial Hemiatrophies, Facial Hemiatrophies Progressive, Facial hemiatrophy, Facial hemiatrophy (disorder), Facial Hemiatrophy of Romberg, Facial Hemiatrophy Progressive, Facial hemiatrophy RETIRED, Facial trophoneurosis, Hemiatrophies Facial, Hemiatrophies Progressive Facial, hemiatrophy face, Hemiatrophy Facial, Hemiatrophy Progressive Facial, Hemifacial Atrophies, Hemifacial Atrophies Progressive, Hemifacial Atrophy, HEMIFACIAL ATROPHY PROGRESSIVE, hemifacial atrophy Romberg, HFA, Parry Romberg, Parry Romberg Disease, Parry Romberg Syndrome, Parry Romberg's disease, PARRY ROMBERY DIS, Progressive Facial Hemiatrophies, Progressive Facial Hemiatrophy, Progressive Hemifacial Atrophies, Progressive Hemifacial Atrophy, Romberg, ROMBERG DIS, ROMBERG DISEASE, Romberg Facial Hemiatrophy, ROMBERGS DIS, Rombergs Disease, Romberg's Disease, Romberg's syndrome, Romberg's trophoneurosis, Syndrome Parry Romberg, Synonym/Hemiatrophy, face, Synonym/HFA, Synonym/Parry-Romberg syndrome, Synonym/Progressive hemifacial atrophy, Synonym/PRS, Synonym/Romberg's syndrome
Treatment
Other Treatments
TX/Constitutional/No definitive treatment
Definition

A syndrome characterized by slowly progressive unilateral atrophy of facial subcutaneous fat, muscle tissue, skin, cartilage, and bone; The condition typically progresses over a period of 2-10 years and then stabilizes; Parry Romberg Syndrome; HFA; PRS; Progressive Facial Hemiatrophy;

Progressive Hemifacial Atrophy; Romberg Syndrome;

Parry-Romberg syndrome is a rare disorder characterized by slowly progressive degeneration (atrophy) of the soft tissues of half of the face (hemifacial atrophy); Some individuals may experience distinctive changes of the eyes and hair; and neurological abnormalities including episodes of uncontrolled electrical disturbances in the brain (seizures) and episodes of severe pain in tissues supplied by the fifth cranial nerve (trigeminal nerve) including the mouth, cheek, nose, and/or other facial tissues (trigeminal neuralgia); Symptoms and physical findings associated with Parry-Romberg syndrome usually become apparent during the first or early during the second decade of life;

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External Links Related to Facial hemiatrophy, progressive (Parry-Romberg)
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NEJM (The New England Journal of Medicine)
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