Disease Information for Erythroderma desquamativatum, infants

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Clinical Manifestations
Signs & Symptoms
Scaling/Skin finding
Neonatal edema/anasarca
Demographics & Risk Factors
Population Group
Child
Infant
Population/Pediatrics population
Sex & Age Groups
Population/Child
Population/Child-Infant Only
Population/Children/all
Population/Infant
Associated Diseases & Rule outs
Associated Disease & Complications
Erythroderma desquamativatum, infants
Neonatal Erythroderma
Disease Mechanism & Classification
Class
CLASS/Pediatric disorders (ex)
CLASS/Dermatologic/Subcutaneous (category)
CLASS/Skin disorder (ex)
Process
PROCESS/Reference organ/system (category)
Synonyms
Synonym
Erythroderma desquamativatum infants, Synonym/Leiner's disease
Definition

Leiner"s disease; Leiner’s syndrome; Erythrodermia desquamativa Leiner; Leiner-Moussous disease; Dermatitis exfoliativa generalisata; desquamative erythrodermia in infants; eczema universale seborrheicum; erythrodermia desquamativa in infants; erythroderma desquamativum; erythrodermic seborrhoic dermatitis in the trianon of life; érythrodermie desquamative des nourrisons (French); exfoliative dermatitis; seborrhoic diathesis in infants;

Syndrome characterised by desquamation (severe generalised seborrhoeic dermatitis), recurrent local and systemic infection, severe diarrhoea, marked wasting and central nervous system deficiency, and failure to thrive; It begins as seborrhoic eczematoid lesions of the scalp and face or the gluteal region, eventually spreading to other areas; Keratitis and corneal ulcers may occur; Due to complement C5 deficiency in infancy; Prevalent in infant females; rapid onset in 2nd to 4th month of life; Breast-fed infants are most frequently affected-------[whonamedit_com 2005]----------------------------------------------------------------

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NEJM (The New England Journal of Medicine)
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