Disease Information for Encephalitis, Dawsons/inclusion body
Bodechtel Guttman, Dawson, Dawson encephalitis, Dawson's encephalitis, Dawson's inclusion body encephalitis, DEMENTIA DECEREBRATE, ENCEPH INCLUSION BODY MEASLES, encephalitis Dawson, Encephaltis Inclusion Body Measles, Immunosuppressive measles encephalitis, INCLUSION BODY ENCEPH MEASLES, Inclusion Body Encephalitis Measles, leukencephalitis subacute sclerosing, leukencephalitis Van Bogaert, LEUKOENCEPH SUBACUTE SCLEROSING, LEUKOENCEPH VAN BOGAERTS, Leukoencephalitides Subacute Sclerosing, Leukoencephalitis Subacute Sclerosing, Leukoencephalitis Van Bogaert, Leukoencephalitis Van Bogaerts, Leukoencephalitis Van Bogaert's, MEASLES INCLUSION BODY ENCEPH, Measles inclusion body encephalitis, Measles inclusion body encephalitis (disorder), MIBE Measles inclusion body encephalitis, PANENCEPH SUBACUTE SCLEROSING, Panencephalitides Subacute Sclerosing, PANENCEPHALITIS SUBACUTE SCLEROSING, SCLEROSING LEUKOENCEPH SUBACUTE, Sclerosing Leukoencephalitides Subacute, Sclerosing Leukoencephalitis Subacute, SCLEROSING PANENCEPH SUBACUTE, Sclerosing Panencephalitides Subacute, Sclerosing Panencephalitis Subacute, SSPE, SSPE Sbacut sclros panenceph, SSPE Subacute sclerosing panencephalitis, Subacut sclerosing panencephal, subacute inclusion body encephalitis, subacute sclerosing leukencephalitis, Subacute Sclerosing Leukoencephalitides, Subacute Sclerosing Leukoencephalitis, subacute sclerosing leukoencephalopathy, SUBACUTE SCLEROSING PANENCEPH, Subacute Sclerosing Panencephalitides, Subacute sclerosing panencephalitis, Subacute sclerosing panencephalitis (disorder), Subacute sclerosing panencephalitis (SSPE), Van Bogaert, Van Bogaert leukencephalitis, Van Bogaert Leukoencephalitis, VAN BOGAERTS LEUKOENCEPH, Van Bogaerts Leukoencephalitis, Van Bogaert's Leukoencephalitis, Van Bogaert's sclerosing leucoencephalitis, van Bogaert's sclerosing leukoencephalitis, Van Bogaert's sclerosing leukoencephalitis (disorder)
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Bodechtel Guttman, Dawson, Dawson encephalitis, Dawson's encephalitis, Daws... (more)
A lethal subacute progressive dementia of childhood caused by measles viral mutation; school age males with history of previous measles infection two years previous present with bizarre behavior then cognitive, visual, and gait problems; most die in a year; diagnosis by csf antibodies to measles virus; intraventricular interferon slows the course
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A lethal subacute progressive dementia of childhood caused by measles viral... (more) (edit)
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Demographics & Risk Factors[next]
- Travel, Geographic & Climate Related Factors
- Past History
- Population Group
- Population/Inadequate vaccinations/immunizations
- Population/Pediatrics population
- Population/Previously well
- Population/Third world countries
- Sex & Age Groups
- Population/Child
- Population/Child-Infant Only
- Population/Children/all
- Population/Male
- Population/Preschool child/boy
- Population/Pre-teen
Clinical Manifestations[previous][top][next]
- Typical Clinical Presentation
- Presentation/Acute encephalopathy/child
- Presentation/Mental retardation progressive
- Presentation/Progressive dementia/child/infant
- Disease Progression
- Course/Acute
- Course/Chronic disorder
- Course/Lethal
- Course/Median survival 1 year
- Course/Progressive
- Course/Progressive/slowly chronic illness
- Course/Relentless
- Course/Subacute
- Onset/Acute/Course chronic
- Onset/insidious
- Signs & Symptoms
- Child
- Abnormal movements/involuntary
- Altered mental status/Mental status change
- Ataxia
- Behavior problems
- Chorea signs
- CNS symptoms/signs
- Cognitive defect
- Coordination/signs
- Decerebrate posture
- Delayed speech/language development
- Delirium
- Delirium/Agitated delirium
- Gait disturbance/abnormality
- Headache
- Headache in children
- Idiocy/signs
- Impaired judgement/signs
- Involuntary movements
- Irritability/short tempered
- Limb Ataxia
- Limb ataxia/clumsiness child
- Mental slowing/deteriation
- Motor slowing
- Movement or gait disorder/signs
- Multifocal neurologic deficit/signs
- Myoclonus/Myoclonic jerks on exam
- Near recall/memory deficit/defect
- Obtunded/poorly responsive status/signs
- Progressive neurological disorder/signs
- Rapidly progressive dementia
- Seizures
- Stupor/poor reponse to stimulus
- Sudden unconsciousness
- Unconscious/Narcosis status
- Queer bizarre behavior/change
- Delayed speech development/impediment
- Urinary incontinence in Children
- Acutely ill patient/signs
- Fatigue/chronic
- Fatigue/tiredness/exhaustion
- Fever
- High body temperature
- Infant peevish/irritable/fretful
- School/job performance decline
- Vision Loss
- Visual acuity decreasing
- Typical Clinical Presentation
Laboratory Tests[previous][top][next]
- Microbiology & Serology Findings
- Abnormal Lab Findings (Non Measured)
- Abnormal Lab Findings - Increased
Diagnostic Test Results[previous][top][next]
- Other Tests & Procedures
- Pathology
- Electrodiagnosis
- CT Scan
- CT Scan/Head Cortical atrophy
- CT Scan/Head Enlarged brain ventricles
- MRI/Head Brain Abnormal
- MRI/Head Cortical atrophy
- MRI/Head Demyelination white matter
- MRI/Head Grey matter degeneration
- MRI/Head multifocal low density lesions/white matter
- MRI/Head Ventricular enlargement
- MRI/Head White matter lesions
Associated Diseases & Rule outs[previous][top][next]
- Associated Disease & Complications
- Cerebral cortical atrophy
- Cerebral edema
- CNS disease/involvement
- Coma in Children
- Coma/Unconscious
- Convulsions (grand mal)
- Cortical blindness
- Dementia
- Dementia, terminal
- Encephalitis, secondary
- Encephalitis, viral
- Encephalitis/Dawsons inclusion body
- Hallucinations
- Meningitis, chronic
- Paralysis
- Vegetative state/status
- Visual acuity loss
- Cerebral Dysgenesis
- Demyelinating Disease
- Associated Disease & Complications
Disease Mechanism & Classification[previous][top][next]
- Specific Agent
- AGENT/Virus (category)
- Class
- CLASS/Pediatric disorders (ex)
- CLASS/Brain/CNS disorder (ex)
- CLASS/Neurologic (category)
- Pathophysiology
- Pathophysiology/Measles viral replic/def RNA messenger
- Pathophysiology/Neurodevelopmental disorders
- Pathophysiology/Cerebral demyelination
- Pathophysiology/Demyelination
- Pathophysiology/Deranged/CNS immune response/Measles virus
- Pathophysiology/Multifocal cortical pathology
- Pathophysiology/Neurologic degenerative disorder (ex)
- Pathophysiology/Panencephalic process (white and grey)
- Pathophysiology/Immune physiology/defective
- Process
- PROCESS/Allergy/collagen/autoimmune (category)
- PROCESS/INCIDENCE/Extremely rare disease
- PROCESS/Infection/agent specific (category)
- PROCESS/Inflammatory/Granulomatous disorder (category)
- PROCESS/Inflammatory/infection (ex)
- PROCESS/Post-infectious disorder (ex)
- Specific Agent
-
- Synonym
- Synonym/Dawson's encephalitis
- Synonym/Decerebrate dementia syndrome (SSPE)
- Synonym/Encephalitis, inclusion body
- Synonym/Panencephalitis, subacute sclerosing
- Synonym/SSPE
- Synonym/Subacute sclerosing panencephalitis
- Synonym
Treatment[previous][top][next]
- Drug Therapy - Indication
- RX/Amanatadine (Symmetrel)
- RX/Ribavirin (Virazole)
- SX/CNS intraventricular interferon alfa/Isoprinosine po
- Drug Therapy - Indication
External Links Related to Encephalitis, Dawsons/inclusion body[previous][top]
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