Disease Information for Dysplastic Nevus Syndrome, Familal

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Clinical Manifestations
Signs & Symptoms
Brown skin discoloration
Increased pigmentation/tanning/hyperpigmented
Pigmentation Lesions on Healing
Pigmented patches/skin
Associated Diseases & Rule outs
Rule Outs
Melanoma, malignant
Associated Disease & Complications
Congenital nevus
Familial atypical mole syndrome
Hyperpigmentation
Melanoma, malignant
Disease Mechanism & Classification
Class
CLASS/Dermatologic/Subcutaneous (category)
Process
PROCESS/Dysplasia/aplasia (ex)
PROCESS/Hereditofamilial (category)
PROCESS/Hereditofamilial/tumor syndrome (ex)
PROCESS/Neoplastic (category)
PROCESS/Pre-Malignant condition (ex)
PROCESS/Dysplasia disorder/Syndromes (ex)
Synonyms
Synonym
Atypical mole syndrome, Atypical mole syndrome (disorder), B K mole (naevus) syndrome, B K mole (nevus) syndrome, B K mole (nevus) syndrome (disorder), B K Mole Syndrome, Dysplastic naevus syndrome, Dysplastic Nevus Syndrome, Epidermal nevus syndrome, Familial atypical mole malignant melanoma syndrome, Familial atypical mole MM synd, Familial Dysplastic Nevi, FAMMM Fam atyp mole MM synd, FAMMM Familial atypical mole malignant melanoma syndrome, Nevus Syndrome Dysplastic, Schimmelpeming Feurstein Mims Syndrome, Syndrome B K Mole, Syndrome Dysplastic Nevus, Synonym/Dysplastic nevus syndrome
Definition

Atypical Mole Syndrome, familial; B-K Mole Syndrome ; CMM ; Cutaneous Malignant Melanoma, Hereditary ; DNS, Hereditary; Dysplastic Nevus Syndrome ; FAMMM Familial Atypical Mole-Malignant Melanoma Syndrome; HCMM ; Malignant melanoma, Dysplastic Nevus Type.General Discussion: Atypical mole syndrome, also called dysplastic nevus syndrome, is a disorder of the skin characterized by the presence of many mole-like tumors (nevi); Most people have 10-20 moles over their bodies; People with this syndrome often have more than 100 moles, at least some of which are unusual (atypical) in size and structure; These moles vary in size, location, and coloring; They are usually larger than normal moles (5mm or more in diameter) and have irregular borders; Changes in the appearance of these moles must be taken seriously by patients since such changes may foreshadow the onset of cancerous disease; Individuals with atypical mole syndrome are at greater than others for developing cancer of the skin in the form of malignant melanoma; Atypical mole syndrome is thought by some clinicians to be a precursor or forerunner of malignant melanoma; This type of cancer may spread to adjacent parts of the skin or, through the blood and lymph circulation, to other organs;------------------[NORD 2005]----------

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External Links Related to Dysplastic Nevus Syndrome, Familal
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PubMed (National Library of Medicine)
NGC (National Guideline Clearinghouse)
Medscape (eMedicine)
Harrison's Online (accessmedicine)
NEJM (The New England Journal of Medicine)
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