Disease Information for Behcet's Disease: Definition

  • Rare chronic inflammatory disease involving the small blood vessels; It is of unknown etiology and characterized by mucocutaneous ulceration in the mouth and genital region and uveitis with hypopyon; The neuro-ocular form may cause blindness and death; Synovitis, thrombophlebitis, gastrointestinal ulcerations, retinal vasculitis, and optic atrophy may be occur as well;-------------------------

    Behçet"s syndrome; Adamantiades’ syndrome; Adamandiades-Behçet syndrome; Behçet"s aphthae; Behçet"s triple symptom complex; Gilbert"s syndrome; Gilbert-Behçet syndrome; Grande aphtose Touraine; Hulusi Behçet’s syndrome; Morbus Behçet Touraine"s aphthosis; Touraine’s syndrome; Trisymptom Behçet; Cutaneomucouveal syndrome; dermatostomato-ophthalmic syndrome; generalized aphthosis; genito-oral aphthosis with uveitis and hypopyon; hypopyon recedivans; iridocyclitis septica (Gilbert); iritis septica; oculobuccogenital syndrome; iridocyclitis recidivans; iridocyclitis recidivans purulenta; iridocyclitis septica; tridocyclitis with hypopyon; Recurrent systemic disease characterized by uveitis with hypopyon, recurrent ulceration of the mucous membranes of the mouth and pharynx, and ulceration of the genitalia; Joint pain is a trait that usually comes later in the history of the disease than the ulcers of the mouth and genitalia; Iritis frequently is accompanied by conjunctivitis, episcleritis, keratitis, retinal thrombophlebitis, and optic atrophy; The central nervous system, heart, and intestinal tract may be involved; Onset is usually between 10 and 30 years of age, but may occur as late as age 45, and males are affected approximately 5 times more frequently than females; Recurrent every 2 to 3 months and lasting from one week to a month; In some cases it runs a course as long as 20 years; Complete remission is rare; The disorder is chronic and may become fatal when the nervous system is involved;

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